Prevalence of scoliosis in patients with Fontan circulation

TitlePrevalence of scoliosis in patients with Fontan circulation
Publication TypeJournal Article
Year of Publication2013
AuthorsKadhim, M., Pizarro C., Holmes L., Rogers K. J., Kallur A., & Mackenzie W. G.
JournalArchives of disease in childhood
Date Published2013 Mar
KeywordsChild; Child, Preschool; Cohort Studies; Female; Fontan Procedure; Heart Defects, Congenital; Humans; Incidence; Infant; Male; Prevalence; Retrospective Studies; Risk Factors; Scoliosis; Spine

OBJECTIVE: To examine the prevalence of scoliosis in patients with Fontan circulation.
DESIGN: Retrospective cohort (case-only), level IV study.
SETTING: A comprehensive paediatric centre.
METHODS: We examined the radiographs of 194 patients who underwent Fontan completion surgery between 1998 and 2011 at a median age of 1.3 years.
MAIN OUTCOME MEASURE: We collected data on the age at the last available radiograph and when scoliosis was diagnosed; we used the first available radiograph with scoliosis. We also measured the magnitude and direction of the spinal curve in patients with scoliosis.
RESULTS: Median age at radiography was 3.4 years. Nineteen patients (9.8%) developed scoliosis; none of them underwent thoracotomy. Most of the patients with scoliosis were older than 5 years of age at scoliosis diagnosis and the female to male ratio was 5 : 3. The major curve was right thoracic in 12 patients (63.2%), left thoracic in four patients (21.1%) and high thoracic in three patients (15.8%). For every 1 year increase in age there was a 27% increased risk of developing scoliosis.
CONCLUSIONS: There was a high prevalence of scoliosis in patients with Fontan circulation. We recommend interdisciplinary monitoring of these patients to diagnose spinal curve deformities in a timely manner.

Alternate JournalArch. Dis. Child
Refereed DesignationRefereed